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Systemic capillary leak syndrome

ORPHA:188 · Disease · Disorder

HPO 表現型(共 23 項)

Very frequent (99-80%)(2)

  • Increased total leukocyte countHP:0001974
  • Pedal edemaHP:0010741

Frequent (79-30%)(10)

  • Abdominal painHP:0002027
  • Constitutional symptomHP:0025142
  • DiarrheaHP:0002014
  • FatigueHP:0012378
  • HypotensionHP:0002615
  • MyalgiaHP:0003326
  • PancreatitisHP:0001733
  • Pulmonary edemaHP:0100598
  • RhinorrheaHP:0031417
  • Weight lossHP:0001824

Occasional (29-5%)(11)

  • Abnormal renal tubule morphologyHP:0000091
  • ArrhythmiaHP:0011675
  • Cardiorespiratory arrestHP:0006543
  • CoughHP:0012735
  • Multiple myelomaHP:0006775
  • MyocarditisHP:0012819
  • OliguriaHP:0100520
  • PericarditisHP:0001701
  • Pleural effusionHP:0002202
  • Renal insufficiencyHP:0000083
  • Venous thrombosisHP:0004936