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Idiopathic pulmonary fibrosis

ORPHA:2032 · Disease · Disorder

HPO 表現型（共 20 項）

Very frequent (99-80%)(1)

  • Abnormal pulmonary interstitial morphologyHP:0006530

Frequent (79-30%)(16)

  • AcrocyanosisHP:0001063
  • BronchiectasisHP:0002110
  • Clubbing of fingersHP:0100759
  • CoughHP:0012735
  • CracklesHP:0030830
  • Decreased DLCOHP:0045051
  • Exertional dyspneaHP:0002875
  • FatigueHP:0012378
  • Gastroesophageal refluxHP:0002020
  • Ground-glass opacificationHP:0025179
  • Honeycomb lungHP:0025175
  • Pulmonary fibrosisHP:0002206
  • Reduced forced vital capacityHP:0032341
  • Reticular pattern on pulmonary HRCTHP:0025390
  • Subpleural honeycombingHP:0031631
  • Usual interstitial pneumoniaHP:0031950

Occasional (29-5%)(3)

  • Exercise intoleranceHP:0003546
  • OrthodeoxiaHP:0033367
  • Pulmonic regurgitationHP:0010444