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Autoimmune hepatitis
ORPHA:2137 · Disease · Disorder
HPO 表現型(共 34 項)
Obligate (100%)(2)
- Increased circulating IgG concentrationHP:0003237
- Increased circulating immunoglobulin concentrationHP:0010702
Very frequent (99-80%)(7)
- Anti-liver cytosolic antigen type 1 antibody positivityHP:0030909
- Anti-smooth muscle antibody positivityHP:0003262
- Antineutrophil antibody positivityHP:0003453
- Antinuclear antibody positivityHP:0003493
- Elevated circulating hepatic transaminase concentrationHP:0002910
- Liver kidney microsome type 1 antibody positivityHP:0030908
- RosetteHP:0031925
Frequent (79-30%)(6)
- Abdominal painHP:0002027
- Anti-asialoglycoprotein receptor antibody positivityHP:0032469
- ArthralgiaHP:0002829
- Chronic fatigueHP:0012432
- DepressionHP:0000716
- Spider hemangiomaHP:0012522
Occasional (29-5%)(16)
- Acute hepatitisHP:0200119
- AnxietyHP:0000739
- ArthritisHP:0001369
- AscitesHP:0001541
- CirrhosisHP:0001394
- Diffuse hepatic steatosisHP:0006555
- Gastrointestinal hemorrhageHP:0002239
- GlomerulonephritisHP:0000099
- Increased total bilirubinHP:0003573
- Inflammation of the large intestineHP:0002037
- JaundiceHP:0000952
- Sclerosing cholangitisHP:0030991
- SplenomegalyHP:0001744
- ThyroiditisHP:0100646
- Ulcerative colitisHP:0100279
- VitiligoHP:0001045
Very rare (<4-1%)(3)
- Fulminant hepatitisHP:0004787
- Hepatocellular carcinomaHP:0001402
- Viral hepatitisHP:0006562