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Felty syndrome

ORPHA:47612 · Disease · Disorder

HPO 表現型(共 36 項)

Very frequent (99-80%)(12)

  • Abnormal joint morphologyHP:0001367
  • ArthralgiaHP:0002829
  • ArthritisHP:0001369
  • AutoimmunityHP:0002960
  • Decreased total neutrophil countHP:0001875
  • ImmunodeficiencyHP:0002721
  • Limitation of joint mobilityHP:0001376
  • OsteolysisHP:0002797
  • Recurrent infectionsHP:0002719
  • Recurrent respiratory infectionsHP:0002205
  • Subcutaneous noduleHP:0001482
  • SynovitisHP:0100769

Frequent (79-30%)(10)

  • Abnormal lymphocyte morphologyHP:0004332
  • AnemiaHP:0001903
  • Chronic otitis mediaHP:0000389
  • LymphadenopathyHP:0002716
  • Recurrent pharyngitisHP:0100776
  • Recurrent pneumoniaHP:0006532
  • RhinitisHP:0012384
  • SinusitisHP:0000246
  • SplenomegalyHP:0001744
  • Weight lossHP:0001824

Occasional (29-5%)(14)

  • Bone marrow hypocellularityHP:0005528
  • CellulitisHP:0100658
  • EpiscleritisHP:0100534
  • Generalized hyperpigmentationHP:0007440
  • HepatomegalyHP:0002240
  • Irregular hyperpigmentationHP:0007400
  • LymphomaHP:0002665
  • PericarditisHP:0001701
  • Peripheral neuropathyHP:0009830
  • PleuritisHP:0002102
  • Pulmonary fibrosisHP:0002206
  • Recurrent urinary tract infectionsHP:0000010
  • SepsisHP:0100806
  • ThrombocytopeniaHP:0001873