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Idiopathic non-lupus full-house nephropathy

ORPHA:567544 · Clinical syndrome · Disorder

HPO 表現型（共 22 項）

Very frequent (99-80%)(1)

  • ProteinuriaHP:0000093

Frequent (79-30%)(6)

  • Decreased circulating complement C3 concentrationHP:0005421
  • Decreased circulating complement C4 concentrationHP:0045042
  • HypertensionHP:0000822
  • Nephrotic syndromeHP:0000100
  • Reduced circulating complement concentrationHP:0004431
  • Renal insufficiencyHP:0000083

Occasional (29-5%)(11)

  • Abnormal glomerular mesangium morphologyHP:0001966
  • Acute kidney injuryHP:0001919
  • ArthritisHP:0001369
  • Elevated circulating creatinine concentrationHP:0003259
  • Glomerular C3 depositionHP:0012576
  • GlomerulonephritisHP:0000099
  • Microscopic hematuriaHP:0002907
  • Oral ulcerHP:0000155
  • SerositisHP:0045073
  • Skin rashHP:0000988
  • SynovitisHP:0100769

Very rare (<4-1%)(2)

  • Abnormality of the immune systemHP:0002715
  • Abnormality of the nervous systemHP:0000707

Excluded (0%)(2)

  • Anti-dsDNA antibody positivityHP:0020151
  • AutoimmunityHP:0002960