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Polyarteritis nodosa

ORPHA:767 · Disease · Disorder

HPO 表現型(共 28 項)

Very frequent (99-80%)(1)

  • Abnormal skin morphologyHP:0011121

Frequent (79-30%)(10)

  • Abnormality of the kidneyHP:0000077
  • ArthralgiaHP:0002829
  • Elevated circulating C-reactive protein concentrationHP:0011227
  • FeverHP:0001945
  • Livedo racemosaHP:0033260
  • MyalgiaHP:0003326
  • Peripheral neuropathyHP:0009830
  • Polyarticular arthritisHP:0005764
  • PolyneuritisHP:0031003
  • Weight lossHP:0001824

Occasional (29-5%)(14)

  • Abdominal painHP:0002027
  • Abnormal cardiovascular system morphologyHP:0030680
  • Abnormal lung morphologyHP:0002088
  • Abnormality of the gastrointestinal tractHP:0011024
  • Abnormality of the nervous systemHP:0000707
  • Cutis marmorataHP:0000965
  • ErythemaHP:0010783
  • HypertensionHP:0000822
  • Morphological central nervous system abnormalityHP:0002011
  • PericarditisHP:0001701
  • Raynaud phenomenonHP:0030880
  • Sensory axonal neuropathyHP:0003390
  • Skin ulcerHP:0200042
  • Subcutaneous noduleHP:0001482

Very rare (<4-1%)(3)

  • Abnormality of the eyeHP:0000478
  • CardiomyopathyHP:0001638
  • PleuritisHP:0002102