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Lymphoid interstitial pneumonia
ORPHA:79128 · Disease · Disorder
HPO 表現型(共 34 項)
Very frequent (99-80%)(1)
- CoughHP:0012735
Frequent (79-30%)(16)
- Autoimmune antibody positivityHP:0030057
- AutoimmunityHP:0002960
- ClubbingHP:0001217
- CracklesHP:0030830
- Decreased DLCOHP:0045051
- DyspneaHP:0002094
- Eczematoid dermatitisHP:0000964
- Failure to thriveHP:0001508
- FatigueHP:0012378
- Ground-glass opacificationHP:0025179
- HypoxemiaHP:0012418
- Multiple pulmonary cystsHP:0005948
- Parenchymal consolidationHP:0032177
- Restrictive ventilatory defectHP:0002091
- Severe viral infectionHP:0031691
- WheezingHP:0030828
Occasional (29-5%)(16)
- Abnormality of connective tissueHP:0003549
- BronchiectasisHP:0002110
- Centrilobular ground-glass opacification on pulmonary HRCTHP:0025180
- Enlarged kidneyHP:0000105
- FeverHP:0001945
- HepatomegalyHP:0002240
- ImmunodeficiencyHP:0002721
- Keratoconjunctivitis siccaHP:0001097
- Mediastinal lymphadenopathyHP:0100721
- Pulmonary venous hypertensionHP:0030950
- Raynaud phenomenonHP:0030880
- Respiratory tract infectionHP:0011947
- Rheumatoid arthritisHP:0001370
- Skin rashHP:0000988
- Subpleural interstitial thickeningHP:0025178
- Weight lossHP:0001824
Very rare (<4-1%)(1)
- Pulmonary fibrosisHP:0002206