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Lymphoid interstitial pneumonia

ORPHA:79128 · Disease · Disorder

HPO 表現型(共 34 項)

Very frequent (99-80%)(1)

  • CoughHP:0012735

Frequent (79-30%)(16)

  • Autoimmune antibody positivityHP:0030057
  • AutoimmunityHP:0002960
  • ClubbingHP:0001217
  • CracklesHP:0030830
  • Decreased DLCOHP:0045051
  • DyspneaHP:0002094
  • Eczematoid dermatitisHP:0000964
  • Failure to thriveHP:0001508
  • FatigueHP:0012378
  • Ground-glass opacificationHP:0025179
  • HypoxemiaHP:0012418
  • Multiple pulmonary cystsHP:0005948
  • Parenchymal consolidationHP:0032177
  • Restrictive ventilatory defectHP:0002091
  • Severe viral infectionHP:0031691
  • WheezingHP:0030828

Occasional (29-5%)(16)

  • Abnormality of connective tissueHP:0003549
  • BronchiectasisHP:0002110
  • Centrilobular ground-glass opacification on pulmonary HRCTHP:0025180
  • Enlarged kidneyHP:0000105
  • FeverHP:0001945
  • HepatomegalyHP:0002240
  • ImmunodeficiencyHP:0002721
  • Keratoconjunctivitis siccaHP:0001097
  • Mediastinal lymphadenopathyHP:0100721
  • Pulmonary venous hypertensionHP:0030950
  • Raynaud phenomenonHP:0030880
  • Respiratory tract infectionHP:0011947
  • Rheumatoid arthritisHP:0001370
  • Skin rashHP:0000988
  • Subpleural interstitial thickeningHP:0025178
  • Weight lossHP:0001824

Very rare (<4-1%)(1)

  • Pulmonary fibrosisHP:0002206