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Psoriasis-related juvenile idiopathic arthritis

ORPHA:85436 · Disease · Disorder

HPO 表現型(共 29 項)

Very frequent (99-80%)(1)

  • Abnormality of tumor necrosis factor secretionHP:0011118

Frequent (79-30%)(12)

  • Antinuclear antibody positivityHP:0003493
  • ArthralgiaHP:0002829
  • ArthritisHP:0001369
  • AutoimmunityHP:0002960
  • EnthesitisHP:0100686
  • Finger dactylitisHP:0031090
  • Nail pitsHP:0001803
  • OligoarthritisHP:0040313
  • Polyarticular arthritisHP:0005764
  • PruritusHP:0000989
  • Psoriasiform dermatitisHP:0003765
  • Toe dactylitisHP:0031091

Occasional (29-5%)(11)

  • Abnormal shoulder morphologyHP:0003043
  • Abnormality of the kneeHP:0002815
  • Abnormality of the wristHP:0003019
  • Anterior uveitisHP:0012122
  • Generalized morning stiffnessHP:0005197
  • Limitation of joint mobilityHP:0001376
  • Malar rashHP:0025300
  • Psoriasiform lesionHP:0025526
  • Reduced visual acuityHP:0007663
  • Skin rashHP:0000988
  • UveitisHP:0000554

Very rare (<4-1%)(5)

  • Abnormality of the temporomandibular jointHP:0010754
  • IridocyclitisHP:0001094
  • IritisHP:0001101
  • OnycholysisHP:0001806
  • Sacroiliac arthritisHP:0012317